| 產(chǎn)品詳情 |
| Edit |   |
|---|
| Antigenic Specificity | GALNS |
|---|
| Clone | polyclonal |
|---|
| Host Species | Goat |
|---|
| Reactive Species | human |
|---|
| Isotype | n/a |
|---|
| Format | purified |
|---|
| Size | 100 ug |
|---|
| Concentration | n/a |
|---|
| Applications | peptide-ELISA: 1:64000, Western Blot: 0.01-0.03 μg/mL |
|---|
| Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
|---|
| Description | GALNS Polyclonal Antibody. This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans, keratan sulfate, and chondroitin 6-sulfate. Sequence alterations including point, missense and nonsense mutations, as well as those that affect splicing, result in a deficiency of this enzyme. Deficiencies of this enzyme lead to Morquio A syndrome, a lysosomal storage disorder. |
|---|
| Immunogen | n/a |
|---|
| Other Names | GALNS; galactosamine (N-acetyl)-6-sulfate sulfatase (Morquio syndrome, mucopolysaccharidosis type IVA); GALNAC6S; GAS; MPS4A; N-acetylgalactosamine-6-sulfatase; chondroitinase |
|---|
| Gene, Accession # | Entrez: 2588; Uniprot: P34059 |
|---|
| Catalog # | PA5-18808 |
|---|
| Price | |
|---|
| Order / More Info | GALNS Antibody from INVITROGEN ANTIBODIES |
|---|
| Product Specific References | n/a |
|---|
| 產(chǎn)品資料 |
|
|