| 產(chǎn)品詳情 |
| Edit |   |
|---|
| Product Name | ACADSB, 34-432aa, Human, His tag, E.coli |
|---|
| Description | Purity: > 90% by SDS - PAGE Format: Liquid. In 20mM Tris-HCl buffer (pH 8.0) containing 0.1M NaCl, 10% glycerol,1mM DTT. Short/branched chain specific acyl-CoA dehydrogenase(ACADSB), is a member of the acyl-CoA dehydrogenase family of enzymes that catalyze the dehydrogenation of acyl-CoA derivatives in the metabolism of fatty acids or branch chained amino acids. ACADSB catalyzes the degradation of L-isoleucine and has the highest affinity for (s)-2-methylbutyryl-CoA, isobutyryl-CoA and 2-methylhexanoyl-CoA as substrates. Defects in ACADSB are the cause of short/branched-chain acyl-CoA dehydrogenase deficiency (SBCADD), an autosomal recessive disorder characterized by an increase of 2-methylbutyrylglycine and 2-methylbutyrylcarnitine in blood and urine. Recombinant human ACADSB protein, fused to His-tag at N-terminus, was expressed in E.coli and purified by using conventional chromatography techniques. |
|---|
| Size | 250ug, 50ug, 10ug |
|---|
| Concentration | n/a |
|---|
| Applications | SDS-PAGE |
|---|
| Other Names | Short/branched chain specific acyl-CoA dehydrogenase mitochondrial, Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial, 2-MEBCAD, ACAD7, SBCAD |
|---|
| Gene, Accession, CAS # | NP 001600 |
|---|
| Catalog # | ATGP1628 |
|---|
| Price | |
|---|
| Order / More Info | ACADSB, 34-432aa, Human, His tag, E.coli from ATGen |
|---|
| Product Specific References | n/a |
|---|
| 產(chǎn)品資料 |
|
|